Congenital Pseudarthrosis of the Tibia: A Rare Orthopaedic Entity-A Focused Review
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Abstract
Congenital pseudarthrosis of the tibia (CPT) is a rare childhood disorder that may begin as anterolateral bowing and progress to established false-joint nonunion, refracture, limb-length discrepancy and disability. This focused review summarizes the clinical relevance, proposed pathophysiology, association with neurofibromatosis type 1, imaging findings, and treatment principles of CPT. Careful distinction between precursor bowing and established pseudarthrosis is emphasized, and an individualized multidisciplinary approach is recommended.
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