An uncommon “third window” in retrofenestral otosclerosis

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Global Journal of Medical and Clinical Case Reports volume9-issue4 articles
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Submitted: October 27, 2022
Published: Nov 9, 2022
DOI: 10.17352/2455-5282.000162
Keywords:
Otosclerosis, Cavitating otosclerosis, Diverticulum of internal auditory canal, Third window, Gusher

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Zambonini Giulia*
Department of Otorhinolaryngology, “Guglielmo da Saliceto” Hospital, Piacenza, Italy
Ghiselli Sara
Department of Otorhinolaryngology, “Guglielmo da Saliceto” Hospital, Piacenza, Italy
Di Trapani Giuseppe
Department of Otorhinolaryngology, “Guglielmo da Saliceto” Hospital, Piacenza, Italy
Maroldi Roberto
DSMC, University of Brescia, Italy
Cuda Domenico
Department of Otorhinolaryngology, “Guglielmo da Saliceto” Hospital, Piacenza, Italy

Abstract

Otosclerosis is an otologic disease characterized by disordered resorption and deposition of the otic capsule bone. It can lead to progressive conductive, mixed or sensorineural Hearing Loss (HL). In rare cases, it manifests itself with a tendency for massive bone resorption with subsequent formation of cavities (“cavitating otosclerosis”). Cavities can sometimes realize communication between the Cerebrospinal Fluid (CSF) at the Internal Auditory Canal (IAC) and the cochlear duct. In these uncommon cases, a “third-window” phenomenon may be established as a concomitant cause of conductive HL. Therefore, the feasibility of stapes surgery should be evaluated, without underestimating the risk of gusher complications.


In this report, we discuss the case of a female patient affected by cavitating otosclerosis realizing a connection between IAC and cochlear duct, with mixed hearing loss.

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Article Details

Giulia, Z., Sara, G., Giuseppe, D. T., Roberto, M., & Domenico, C. (2022). An uncommon “third window” in retrofenestral otosclerosis. Global Journal of Medical and Clinical Case Reports, 9(4), 063–067. https://doi.org/10.17352/2455-5282.000162
Case Reports

Copyright (c) 2022 Zambonini G, et al.

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This work is licensed under a Creative Commons Attribution 4.0 International License.

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